Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns
https://doi.org/10.15789/1563-0625-SOI-1930
Abstract
Hereditary angioedema (HAE) is a genetically caused orphan disease with a high risk of developing life-threatening attacks, thus requiring availability for up-to-date information on this problem for the doctors of any specialties. A limited number of observations determine the value of the analysis for each clinical case. Many facets of clinical manifestations, a list of predisposing and triggering factors, as well as limitations of some diagnostic and therapeutic algorithms, require the development of individual management schemes under distinct clinical situations. In this paper, we present the unique clinical cases with certain limitations, describing unexpected onset of the disease in the course of pregnancy, management aspects during delivery and post-delivery periods in a women with a previously confirmed HAE diagnosis. Adapted diagnostic algorithms of postnatal diagnostic verification are presented for children with burdened genetic history. We express some assumptions about involvement of a multidisciplinary team of specialists, personalized approach to building a management plan with an “online” correction depending on observation stage of НАЕ patient.
About the Authors
E. N. Bobrikova
Сlinical Hospital No. 52
Russian Federation
Russian Federation
Chief District Allergologist, Head, Clinical and Diagnostic Center for Allergology and Immunology
Moscow
A. R. Denisova
First Moscow State I. Sechenov Medical University
Russian Federation
Russian Federation
PhD (Medicine), Assistant Professor, Department of Pediatrics, N. Filatov Clinical Institute for Pediatric Health
Moscow
T. S. Kotomina
Сlinical Hospital No. 52
Russian Federation
Russian Federation
PhD (Medicine), The Moscow Doctor, Head, Obstetric Department
Moscow
S. A. Serdotetskova
Сlinical Hospital No. 52
Russian Federation
Russian Federation
Serdotetskova Sofia A. – Allergist-Immunologist, Center for Allergology and Immunology
123182, Moscow, Pekhotnaya str., 3
Phone: 7 (499) 196-45-65
D. S. Fomina
Сlinical Hospital No. 52; First Moscow State I. Sechenov Medical University
Russian Federation
Russian Federation
Phd (Medicine), Chief City AllergologistImmunologist. Associate Professor, Department of Clinical Immunology and Allergology, First Moscow State I. Sechenov Medical University; Head, Allergology and Immunology Center, Сlinical Hospital No. 52
Moscow
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For citations:
Bobrikova E.N., Denisova A.R., Kotomina T.S., Serdotetskova S.A., Fomina D.S. Significance of individual management plan for the patients with hereditary lymphangioedema during pregnancy and lactation, and in newborns. Medical Immunology (Russia). 2020;22(3):577-584. (In Russ.) https://doi.org/10.15789/1563-0625-SOI-1930
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